Diagnostic power of aortic elastic properties in young patients with Marfan syndrome
نویسندگان
چکیده
منابع مشابه
The Characteristics of Acute Aortic Dissection among Young Chinese Patients: A Comparison between Marfan Syndrome and Non-Marfan Syndrome Patients
PURPOSE Aortic dissection (AoD) is one of the most common catastrophes involving the aorta. Nevertheless, early diagnosis remains to be a challenge in the Emergency Department (ED), particularly in young individuals. In this study, we attempted to identify the characteristics of acute AoD among young individuals, particular in patients with Marfan syndrome. MATERIALS AND METHODS This was an r...
متن کاملComparison of aortic root replacement in patients with Marfan syndrome.
OBJECTIVES Although the aortic-valve-sparing (AVS) reimplantation technique according to David has shown favorable durability results in mid-term and long-term studies, composite valve grafting (CVG) according to Bentall is still considered the standard procedure. METHODS Retrospectively, we evaluated the results of aortic root replacement of patients with Marfan syndrome (MFS) who underwent ...
متن کاملTreatment of aortic disease in patients with Marfan syndrome.
Marfan syndrome (MFS) is a heritable disorder of the connective tissue with a prevalence of 1 in 3000 to 5000 individuals. The condition is inherited in an autosomal dominant manner with complete penetrance but demonstrates variable expression with significant intraand interfamilial variation. Approximately 25% of patients do not have a family history and represent sporadic, new mutations for t...
متن کاملMagnetic resonance imaging evaluation of aortic elastic properties as early expression of Marfan syndrome.
In Marfan syndrome, early identification and treatment of aortic involvement could improve prognosis, but clinical diagnosis may be difficult at a young age, before aortic dilation occurs. The aim of this study was to evaluate biomechanical aortic properties in Marfan patients and in their relatives to identify an early index of aortic involvement. A magnetic resonance imaging (MRI) morphologic...
متن کاملAortic elastic properties in patients with bicuspid aortic valve.
e read with great interest the report by Siu and Silversides (1) nd we congratulate the investigators on their intriguing review. n this study, the authors tried to summarize available inforation on pathology, genetics, and clinical aspects of bicuspid ortic valve (BAV) disease. However, due to recent publications n aortic elasticity alterations in BAV disease, we believe that a ew additional c...
متن کاملذخیره در منابع من
با ذخیره ی این منبع در منابع من، دسترسی به آن را برای استفاده های بعدی آسان تر کنید
ژورنال
عنوان ژورنال: The Journal of Thoracic and Cardiovascular Surgery
سال: 2005
ISSN: 0022-5223
DOI: 10.1016/j.jtcvs.2004.07.019